Extramedullary Hematopoiesis in a Man With β-Thalassemia: An Uncommon Cause of an Adrenal Mass

Zeighami, Shahryar; Eslahi, Seyed Ali; Hosseini, Mohammad Mehdi; Ariafar, Ali; Pakbaz, Sara; Rastegari, Mohsen; Khazraei, Hajar

doi:10.17795/acr-29003

Extramedullary Hematopoiesis in a Man With β-Thalassemia: An Uncommon Cause of an Adrenal Mass

Authors

Shahryar Zeighami ¹

Seyed Ali Eslahi

Mohammad Mehdi Hosseini ¹

Ali Ariafar ¹

Sara Pakbaz ²

Mohsen Rastegari ¹

Hajar Khazraei ³

¹ Department of Urology, Shiraz University of Medical Sciences, Shiraz, IR Iran

² Pathology Department, Shiraz University of Medical Sciences, Shiraz, IR Iran

³ Colorectal Research Center, Shiraz University of Medical Sciences, Shiraz, IR Iran

10.17795/acr-29003

Abstract

Introduction Extramedullary hematopoiesis (EMH) commonly occurs in the spleen, liver and lymph nodes. Rare cases of EMH in the adrenal gland have been reported. Case Presentation We report the case of a 33-year-old man from the South of Iran suffering from major β-thalassemia, who underwent open left adrenalectomy and the histopathology revealed EMH. Conclusions In patients in which a history of hematologic disorders exists, careful imaging and hormonal assay should be done to certify a diagnosis of EMH. However, the surgical management becomes inevitable in certain cases.

Keywords

Extramedullary hematopoiesis

Thalassemia

Adrenal